International Bullous Diseases Group: Consensus on Diagnostic Criteria for Epidermolysis Bullosa Acquisita

C. Prost-Squarcioni; F. Caux; E. Schmidt; M.F. Jonkman; S. Vassileva; S.C. Kim; P. Iranzo; M. Daneshpazhooh; J. Terra; J. Bauer; J. Fairley; R. Hall; M. Hertl; J.S. Lehman; B. Marinovic; A. Patsatsi; D. Zillikens; V. Werth; D.T. Woodley; D.F. Murrell


The British Journal of Dermatology. 2018;179(1):30-41. 

In This Article


The IBDG met three times during 2015: at the annual meetings of the American Academy of Dermatology in San Francisco (21 experts from 11 countries); the European Society of Dermatological Research in Rotterdam (11 experts from six countries); and the European Academy of Dermatology and Venereology (EADV) in Copenhagen (22 experts from 14 countries). Initial presentations and discussions took place at the first two meetings. After further revisions and discussions at the third meeting, consensus voting took place on the definitions and diagnostic techniques. We defined 'consensus' according to Harmonize Outcome Measures for Eczema by having less than one–third of the key opinion leaders disagreeing on a given diagnostic criterion.[16,17] Fifty proposals (Table S1; see Supporting Information) were put forward for discussion and voting related to the diagnostic processes involved in EBA. For each proposal, participants could 'agree', be 'undecided' or 'disagree'. Tables summarizing the literature (Tables S2–S6; see Supporting Information) and examples of cases of EBA (Appendix S2; see Supporting Information) were presented for discussion.