Chiari Malformation Associated With Craniosynostosis

Jennifer Strahle, M.D.; Karin M. Muraszko, M.D.; Steven R. Buchman, M.D.; Joseph Kapurch, B.S.; Hugh J. L. Garton, M.D., M.H.Sc.; Cormac O. Maher, M.D.


Neurosurg Focus. 2011;31(3):e2 

In This Article


Chiari malformation is seen frequently in patients with syndromic, multisuture and single-suture synostosis of the lambdoid suture. In some cases, the CM and craniosynostosis present concurrently. In other patients, we have noted the development of CM after the surgical treatment of the craniosynostosis. In patients presenting with both CM and craniosynostosis, we recommend treating the craniosynostosis first, with simultaneous posterior fossa expansion only if there are neurological symptoms or spinal syringes. When CM decompression is not carried out at the time of craniosynostosis repair, it should be considered if neurological symptoms or a spinal syrinx persist after the initial surgery. Neurosurgical follow-up is particularly necessary for patients with multisuture, syndromic, or lambdoid craniosynostosis, as well as for those patients requiring treatment of hydrocephalus.


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