A 3660g full-term infant was born after an uncomplicated pregnancy. A fetal sonogram at 20 weeks had been normal. The child had Apgars of 7 and 8 at 1 and 5min respectively. However at approximately 10min after delivery he became dusky and tachycardic. A chest radiograph was obtained (Figure 1), and subsequently a CT scan (Figures 2 and 3) was obtained. A multiloculated cystic mass was found to be present in the right lower lobe. The patient was taken to the operating room where a thoracotomy was performed.
Anteroposterior chest radiograph. Large air-filled cysts occupy most of the right lung with shift of the mediastinum toward the left.
Sagittal section reformatted showing the right main stem bronchus displaced anteriorly, with the compressed right upper lobe, right middle lobe anteriorly and the collapsed nonaerated right lower lobe posterior and inferior to the large cystic mass.
J Perinatol. 2008;28(1):82-84. © 2008 Nature Publishing Group
Cite this: Neonatal Pleuropulmonary Blastoma, Type 1 - Medscape - Jan 01, 2008.