Abstract and Introduction
A female patient with progressive systemic sclerosis and pulmonary fibrosis had a dermatofibrosarcoma protuberans on the right thigh. After resection of the tumor, new lesions occurred in the scar, and wide excision was repeated. Two years later, a lung metastasis was discovered, and segmental resection was done. After 1 year of follow-up, no local recurrences or metastases were found.
Dermatofibrosarcoma protuberans (DFSP) is a tumor of intermediate malignancy that rarely metastasizes but has a high incidence of local recurrence. Although the lung is the most frequent site of metastasis, there are only a few reports of surgical excision of pulmonary metastases, and cure has rarely been achieved despite resection. We report the case of a female patient with a lung metastasis of DFSP, who was well 1 year after segmental lung resection.
South Med J. 2002;95(3) © 2002 Lippincott Williams & Wilkins
Cite this: Dermatofibrosarcoma Protuberans With Lung Metastasis in a Patient With Progressive Systemic Sclerosis - Medscape - Mar 01, 2002.