Dermatofibrosarcoma Protuberans With Lung Metastasis in a Patient With Progressive Systemic Sclerosis

Gerald W. Westermann, MD, Horst Buerger, MD, Ulrike Kappes, MD, Fritz Matzkies, MD, Klaus Kisters, MD

Disclosures

South Med J. 2002;95(3) 

In This Article

Abstract and Introduction

A female patient with progressive systemic sclerosis and pulmonary fibrosis had a dermatofibrosarcoma protuberans on the right thigh. After resection of the tumor, new lesions occurred in the scar, and wide excision was repeated. Two years later, a lung metastasis was discovered, and segmental resection was done. After 1 year of follow-up, no local recurrences or metastases were found.

Dermatofibrosarcoma protuberans (DFSP) is a tumor of intermediate malignancy that rarely metastasizes but has a high incidence of local recurrence.[1] Although the lung is the most frequent site of metastasis, there are only a few reports of surgical excision of pulmonary metastases, and cure has rarely been achieved despite resection.[2] We report the case of a female patient with a lung metastasis of DFSP, who was well 1 year after segmental lung resection.

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