What are the symptoms of acute hemorrhagic edema of infancy (AHEI) in Henoch-Schönlein purpura (IgA vasculitis)?

Updated: Jan 08, 2021
  • Author: Rajendra Bhimma, MBChB, MD, PhD, DCH (SA), FCP(Paeds)(SA), MMed(Natal); Chief Editor: Craig B Langman, MD  more...
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Answer

Acute hemorrhagic edema of infancy (AHEI) usually occurs in infants aged 4-24 months, often after drug ingestion or infection. Onset is dramatic, with acute palpable purpura, ecchymoses, and tender edema of the limbs and face. Fever, if present, remains mild. Infants remain hemodynamically stable. Dermatologic findings are notable for a cockadelike rosette-shaped pattern of macular-papular-hemorrhagic lesions on the face, auricles, and extremities, which usually appear in successive crops and display varying stages of evolution at any given time.


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