How is clear cell sarcoma differentiated from Wilms tumor on imaging?

Updated: Mar 04, 2019
  • Author: Ali Nawaz Khan, MBBS, FRCS, FRCP, FRCR; Chief Editor: Eugene C Lin, MD  more...
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Answer

Answer

Clear cell sarcoma is a distinct histologic entity that accounts for 4% of the renal tumors observed in childhood. These tumors usually cannot be differentiated from Wilms tumors on images. Clear cell sarcoma is not associated with any other somatic abnormality. Overall, the prognosis is poor compared with that of patients with Wilms tumors. Since bone metastases may occur with this disease, bone scintigraphy or FDG-PET is recommended.


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