What are the clinical phenotypes of relapsing polychondritis (RP)?

Updated: Dec 06, 2018
  • Author: Nicholas Compton, MD; Chief Editor: Herbert S Diamond, MD  more...
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On the basis of a retrospective study of 142 patients with RP, Dion et al proposed that the following three distinct clinical phenotypes of the disease exist [28] :

  • Patients with concomitant myelodysplastic syndrome (MDS) or other hematologic malignancy (< 10% of patients); most are older men; poor prognosis 
  • Patients with tracheobronchial involvement (about 25% of patients)
  • Patients with neither hematologic nor tracheobronchial involvement (about 65% of patients); good prognosis

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