What are the treatment options for functional class IV pulmonary arterial hypertension (PAH)?

Updated: Apr 25, 2018
  • Author: Kristin E Schwab, MD; Chief Editor: Zab Mosenifar, MD, FACP, FCCP  more...
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Answer

Patients with WHO functional class IV disease are typically started on parenteral prostanoid therapy.

For patients who progress or are poorly responsive to initial therapy, practitioners typically add agents from a different class. Agents within the same class (including PDE-5 inhibitors and guanylate cyclase stimulators) should not be used together.

For more details on the specifics of agents within these classes, see the Medication.


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