What are the treatment approach considerations of idiopathic pulmonary arterial hypertension (IPAH)?

Updated: Jul 08, 2020
  • Author: Ronald J Oudiz, MD, FACP, FACC, FCCP; Chief Editor: Zab Mosenifar, MD, FACP, FCCP  more...
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Answer

Treating IPAH requires significant education regarding, and exposure to, the available therapies for IPAH and their potential complications. Because IPAH is relatively rare, management is best left to expert personnel at centers with regular exposure to these patients. Failure to heed this advice can result in medicolegal pitfalls should patient outcome be less than optimal.

A national program designed to develop accredited PH Care Centers (PHCC) has begun, with the goal of raising the overall quality of care and outcomes in patients with PH. [21]

Note that there are no therapies approved for use as primary prevention of IPAH. All approved treatments are for use in patients that have already developed clinical manifestations of IPAH.


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