Which studies are indicated in the workup of idiopathic pulmonary arterial hypertension (IPAH) with comorbidities?

Updated: Jul 08, 2020
  • Author: Ronald J Oudiz, MD, FACP, FACC, FCCP; Chief Editor: Zab Mosenifar, MD, FACP, FCCP  more...
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Answer

Assessment of mechanical lung function can also help differentiate intrinsic pulmonary vascular disease from restrictive or obstructive lung disease. The diffusing capacity of the lung for carbon dioxide (DLCO) is known to decrease in proportion to the degree of IPAH severity.

Sleep apnea must be excluded as a contributor or cause of pulmonary hypertension if the patient's history suggests this diagnosis.

HIV-positive patients have a higher rate of IPAH than the general population; therefore, include an HIV test as part of the routine evaluation.


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