What is the prevalence of eosinophilic granuloma (histiocytosis X) in the US?

Updated: Mar 29, 2018
  • Author: Eleanor M Summerhill, MD, FACP, FCCP; Chief Editor: Zab Mosenifar, MD, FACP, FCCP  more...
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Answer

Pulmonary Langerhans cell histiocytosis X (PLCH) is a rare disorder and the true prevalence is unknown. At 1 specialty referral center in the United States, PLCH was identified in less than 5% of patients who underwent lung biopsy for the diagnosis of interstitial lung disease. [3] At another center, 15 cases of PLCH were found after lung biopsy, compared with 274 cases of sarcoidosis. [4]


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