What are the hereditary syndromes associated with renal cell carcinoma (RCC)?

Updated: May 21, 2019
  • Author: Kush Sachdeva, MD; Chief Editor: E Jason Abel, MD  more...
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Answer

At least four hereditary syndromes associated with renal cell carcinoma are recognized, as follows:

  • von Hippel-Lindau (VHL) syndrome

  • Hereditary papillary renal carcinoma (HPRC)

  • Familial renal oncocytoma (FRO) associated with Birt-Hogg-Dube syndrome (BHDS)

  • Hereditary renal carcinoma (HRC)


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