What is the pathophysiology of neurofibromatosis in renovascular hypertension (RVHT)?

Updated: Dec 01, 2020
  • Author: Rebecca J Schmidt, DO, FACP, FASN; Chief Editor: Vecihi Batuman, MD, FASN  more...
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Answer

Neurofibromatosis

Hypertension in patients with neurofibromatosis is often essential, but some patients also present with RVHT (see the image below). These patients have a pattern of RAS similar to that observed in FMD. However, involvement of the intrarenal arteries and arterioles may also exist. Neurofibromatosis usually involves the renal arteries of both kidneys. [9]

Aortogram of 8-year-old child with neurofibromatos Aortogram of 8-year-old child with neurofibromatosis and renovascular hypertension caused by right renal artery stenosis.

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