What is the prevalence of X-linked spinobulbar muscular atrophy (SBMA) (Kennedy disease)?

Updated: Apr 28, 2014
  • Author: Hidehiro Takei, MD; Chief Editor: Adekunle M Adesina, MD, PhD  more...
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Answer

Answer

Of the hereditary motor neuron diseases (MNDs), X-linked spinobulbar muscular atrophy(SBMA) is one of the least common, with a prevalence of approximately 1 per 40,000 males. Because of a founder effect, SBMA is more common among Japanese and Scandinavian men. [13] In the Vasa region of Western Finland, the prevalence of this condition is reportedly greater than that of ALS, with a prevalence of 13 in 85,000 among the male population. [14]


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