Which patient groups have the highest prevalence of X-linked lymphoproliferative (XLP) syndrome?

Updated: Jan 27, 2019
  • Author: Karen Seiter, MD; Chief Editor: Emmanuel C Besa, MD  more...
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Answer

XLP syndrome has been reported in families of European, African, Asian, and Middle Eastern descent and no evidence exists for a racial or ethnic predilection. Because XLP syndrome is an X-linked disorder, nearly all patients are male. However, a case of a heterozygous female who became symptomatic due to skewed X-chromosome inactivation has been reported. [13, 14]


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