How are malformations of abdominal folds characterized in the treatment of abdominal hernias?

Updated: Jul 23, 2019
  • Author: Assar A Rather, MBBS, MD, FACS; Chief Editor: John Geibel, MD, DSc, MSc, AGAF  more...
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Answer

Pentalogy of Cantrell is a malformation of the upper abdominal fold characterized by an anterior diaphragmatic and pericardial defect, a short bifid sternum, and cardiac defects associated with an epigastric omphalocele sac or hypotrophic epigastric skin. Temporary coverage of the omphalocele during evaluation of the cardiac defects will allow subsequent complete repair of cardiac, diaphragmatic, and pericardial defects.

Vesicointestinal fissure or cloacal exstrophy is a malformation of the lower fold defined by an inferiorly sited omphalocele, exstrophy of the cecum between the hemibladders, diastasis of the symphysis pubis, a short distal colon, no rectum, a shortened small bowel, and occasional meningosacral anomalies. These infants can survive after multiple corrective intestinal and urinary tract procedures.


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