What anomalies are associated with improper development of portions of the abdominal wall in abdominal hernias?

Updated: Jul 23, 2019
  • Author: Assar A Rather, MBBS, MD, FACS; Chief Editor: John Geibel, MD, DSc, MSc, AGAF  more...
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Answer

Improper development of other portions of the abdominal wall leads to specific anomalies. In 1967, Duhamel proposed that maldevelopment of the superior (cephalad) fold of the abdominal wall leads to the thoracic, sternal and diaphragmatic, and abdominal wall defects that make up the upper midline syndrome (pentalogy of Cantrell). This syndrome includes a bifid sternal cleft, an anterior diaphragmatic defect, an anterior pericardial defect, an epigastric omphalocele, and congenital cardiac defects.


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