What is Budd-Chiari syndrome?

Updated: Oct 10, 2018
  • Author: Praveen K Roy, MD, AGAF; Chief Editor: BS Anand, MD  more...
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Answer

Budd-Chiari syndrome is an uncommon condition induced by thrombotic or nonthrombotic obstruction of the hepatic venous outflow and is characterized by hepatomegaly, ascites, and abdominal pain. [49] See the image below.

Sonogram showing hepatic vein thrombus, with new v Sonogram showing hepatic vein thrombus, with new vessels forming. The arrow is pointing to the thrombus.

The prognosis is poor in patients with Budd-Chiari syndrome who remain untreated, with death resulting from progressive liver failure in 3 months to 3 years from the time of the diagnosis. [1] Following portosystemic shunting, however, the 5-year survival rate for patients with the syndrome is 38-87%. The actuarial 5-year survival rate following liver transplantation is 70%. [2, 3, 4]


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