What are the treatment options for Crigler-Najjar syndrome type 1?

Updated: May 21, 2019
  • Author: Hisham Nazer, MBBCh, FRCP, DTM&H; Chief Editor: BS Anand, MD  more...
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Answer

Crigler-Najjar syndrome type 1

  • Pharmacologic therapy - Administration of cholestyramine, calcium phosphate, oral agar, orlistat, and Sn-protoporphyrin [3, 4]

  • Repeated exchange transfusions

  • Long-term phototherapy

  • Plasmapheresis

  • Hemoperfusion

  • Liver transplantation - The only guaranteed form of therapy

  • Hepatocyte transplantation


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