What is dermatofibrosarcoma protuberans (DFSP)?

Updated: Oct 07, 2019
  • Author: Guy J Petruzzelli, MD, PhD, MBA, FACS; Chief Editor: Gregory Gary Caputy, MD, PhD, FICS  more...
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Answer

Answer

Dermatofibrosarcoma protuberans (DFSP) is a slow-growing neoplasm in the dermis that appears as a firm, indurated plaque, usually either red or blue in hue. [78]  DFSP typically appears on the trunk and extremities; however, case reports have shown that DFSP can also occur on the scalp or the face. [79] As the lesion develops, multiple protuberant nodules form within the indurated plaque.

Local recurrence is common because the tumor has microscopic extensions beyond the visible lesion. Therefore, wide excision is recommended for treatment. Mohs surgery has been endorsed as the preferred treatment. DFSP rarely metastasizes. Radiation therapy is not recommended, as it can often elicit more aggressive behavior within the tumor. 


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