What is the role of adrenalectomy in the treatment of other manifestations of McCune-Albright syndrome (MAS)?

Updated: Jan 17, 2019
  • Author: Gabriel I Uwaifo, MD; Chief Editor: George T Griffing, MD  more...
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Answer

The current recommendation for treatment of infantile Cushing syndrome in the context of MAS is bilateral adrenalectomy. Perioperative replacement of hormones is indicated (see Pharmacologic Therapy).

In MAS patients with gigantism or acromegaly, surgical removal should be considered only if the tumor is threatening vision; removal is rarely curative.


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