What is the role of surgery in the treatment of polyostotic fibrous dysplasia (PFD) in McCune-Albright syndrome (MAS)?

Updated: Jan 17, 2019
  • Author: Gabriel I Uwaifo, MD; Chief Editor: George T Griffing, MD  more...
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Answer

Fracture is the primary indication for surgical treatment of dysplastic lesions. Most fractures are treated with traction. However, proximal fractures of the femur may have to be treated with surgically placed fixation devices. [63] Rarely, severe and progressive malformation of the femur can occur. These lesions are usually painful (because of the multiple small fractures associated with them) and may have to be removed surgically. For most PFD lesions, routine removal is not warranted; after removal, the lesion may recur at the same site.

En bloc resection and free metatarsal transfer have been used to treat FD of the fourth metacarpal associated with MAS. [64]


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