What are the International Standard of Care Committee treatment guidelines for respiratory complications in patients with congenital muscular dystrophy?

Updated: Aug 17, 2020
  • Author: Twee T Do, MD; Chief Editor: Jeffrey D Thomson, MD  more...
  • Print

The International Standard of Care Committee consensus recommendations include the following [76] :

  • Regularly scheduled physician visits and patient or family awareness of potential signs and symptoms are elements of a proactive approach to recognize early pulmonary problems prior to the onset of chronic respiratory compromise
  • Pneumococcal and influenza vaccines are suggested for any patient with CMD
  • Palivizumab, a humanized monoclonal antibody against respiratory syncytial virus, should be given to children under 2 years of age as prophylaxis
  • Spinal bracing is required to promote activities of daily living, ensure functional sitting posture, and delay the progression of scoliosis; this allows adequate thoracic growth until optimal timing for spinal surgery
  • Spirometry both in and out of the brace is recommended to evaluate the impact on respiratory function
  • Adjustment is needed between the degree of correction and the compression pressure on the thorax to avoid compromise of respiratory capacity

Did this answer your question?
Additional feedback? (Optional)
Thank you for your feedback!