What are the Endocrine Society, the American Association for Clinical Chemistry, and the European Society of Endocrinology joint treatment guidelines for pheochromocytoma?

Updated: Aug 10, 2018
  • Author: Michael A Blake, MBBCh, MRCPI, FRCR; Chief Editor: George T Griffing, MD  more...
  • Print
Answer

The Endocrine Society, the American Association for Clinical Chemistry, and the European Society of Endocrinology have released clinical practice guidelines for the diagnosis and management of pheochromocytoma and paraganglioma (jointly referred to as PPGL) [32, 33] :

  • Preoperative blockade of hormonally functional PPGL to prevent cardiovascular complications is recommended, along with preoperative medical treatment to normalize blood pressure and heart rate and a high-sodium diet with fluid intake to prevent severe hypotension after removal of the tumor.
  • Blood pressure, heart rate, and glucose levels should be monitored immediately after surgery.
  • Minimally invasive (eg, laparoscopic) adrenalectomy should be performed for most adrenal pheochromocytomas, with open resection reserved for very large or invasive pheochromocytomas; open resection is suggested for paragangliomas, but laparoscopic resection is an option for smaller tumors; partial adrenalectomy is also an option for certain patients.

Did this answer your question?
Additional feedback? (Optional)
Thank you for your feedback!