How prevalent is juvenile xanthogranuloma (JXG) in neurofibromatosis type 1 (NF1)?

Updated: Feb 08, 2019
  • Author: Bhupendra C K Patel, MD, FRCS; Chief Editor: Michael Taravella, MD  more...
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Answer

It is important to realize the relationship of juvenile xanthogranuloma (JXG) with neurofibromatosis type 1 (NF1) and juvenile myelomonocytic leukemia (JMML). JXG can be the presenting sign of NF1. Up to 18% of patients with NF1 younger than 3 years also have JXG.


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