How are PWS in Sturge-Weber syndrome (SWS) treated?

Updated: Dec 26, 2018
  • Author: Masanori Takeoka, MD; Chief Editor: George I Jallo, MD  more...
  • Print
Answer

The PWS needs to be evaluated within the first week of life and differentiated from hemangioma.

Treatment of the cutaneous PWS with dye laser photocoagulation has been helpful in reducing the cosmetic blemish from the cutaneous vascular dilatation. [2] The therapy should start as soon as possible, since multiple treatments are needed and earlier treatment may reduce the number of sessions required. Also, the smaller the lesion is initially, the lower the number of flashes that will be required to remove it. [102, 103]

In a survey of patients with PWS that examined the potential psychological benefits from early treatment of the lesion, Troilius et al found that 75% of the patients reported that the PWS had affected their lives negatively, 62% of them were convinced that their lives would improve if the PWS were removed, 47% of them suffered low self-esteem, and 28% of the patients said that the PWS made their school life and education more difficult. No persistent pigmentation changes or posttreatment scarring were reported after laser therapy. [104]


Did this answer your question?
Additional feedback? (Optional)
Thank you for your feedback!