What are the characteristics of type VIII (periodontal form) Ehlers-Danlos syndrome (EDS)?

Updated: Feb 23, 2021
  • Author: Robert A Schwartz, MD, MPH; Chief Editor: Dirk M Elston, MD  more...
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Answer

Type VIII, the periodontal form, is rare and inherited in an autosomal dominant pattern. Patients with this type have dental involvement with gingival periodontal inflammation. Skin laxity, joint hyperextensibility, and bruisability are variable. Gingival resorption and permanent loss of the teeth are common by the time the patient is aged 30 years.

A review of Ehlers-Danlos syndrome type VIII showed distinctive clinical features. The precise underlying molecular defect is unknown, but patients with this type are similar clinically.


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