What are the diagnostic criteria for febrile ulceronecrotic pityriasis lichenoides?

Updated: Sep 11, 2020
  • Author: Jeffrey P Callen, MD; Chief Editor: Dirk M Elston, MD  more...
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Answer

Constant features are as follows:

  • Fever
  • Acute onset of generalized ulceronecrotic papules and plaques
  • Rapid and progressive course without any tendency to spontaneous resolution
  • Histopathology consistent with PLEVA

Variable features are as follows:

  • Previous history of PLEVA

  • Mucous membrane involvement

  • Systemic involvement

Per the proposed criteria, constant features must be present to establish a definite diagnosis of febrile ulceronecrotic Mucha-Habermann disease. Variable features help to avoid missing cases.


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