What education about cystic fibrosis (CF) should patients and families receive?

Updated: Oct 30, 2018
  • Author: Girish D Sharma, MD, FCCP, FAAP; Chief Editor: Kenan Haver, MD  more...
  • Print
Answer

Provide counseling at the time of initial diagnosis, including information regarding inheritance and risk for recurrence in subsequent pregnancies, and instruct patients and parents regarding appropriate airway clearance technique and the need for chest physical therapy. Also, instruct patients and parents regarding the use of various drug delivery devices, such as valved holding chambers, and nebulizers, and the methods for modifying the pancreatic enzyme dosage.

Discuss when to contact cystic fibrosis center personnel (eg, for acute pulmonary exacerbation or complications) with patients and parents, and be prepared to counsel families regarding the impact of the diagnosis on the emotional life of parents, siblings, and members of the extended family.


Did this answer your question?
Additional feedback? (Optional)
Thank you for your feedback!